The patient had low-set ears, sloping shoulders, a webbed neck and an anti-mongoloid slant of the eyes. His presenting visual acuities were 6/18 and 6/9, in the right and left eyes, respectively. Intraocular pressures were normal.
The right inferotemporal retina (Figures 1 and 2) excluding the macula had gross pigmentary changes. At the 7 o’clock position in the periphery, a small nodule of neovascularization was seen. These features were consistent with spontaneous reattachment of the retina. There was a slight swelling of apparently atypical retinoschisis in the superotemporal periphery from 10 to 12 o’clock. Yellow-white vitreous opacities were also seen.
Examination of the left fundus (Figure 3 and 4) revealed localized inferotemporal dialysis surrounded by minimal subretinal fluid and a well-established demarcation line.